Severe restrictive pulmonary defect in a patient with adult-onset Still's disease.
نویسندگان
چکیده
Adult-onset Still's disease is characterized by seronegative arthritis, fever, and an evanescent skin rash. Earlier reports have described pneumonitis and pleuritis as manifestations of this disease. We report a patient with adult-onset Still's disease with severe restrictive ventilatory impairment and evidence of respiratory muscle weakness who responded to corticosteroid and aspirin therapy.
منابع مشابه
Adult-onset Still's disease with an associated severe restrictive pulmonary defect: a case report.
A 21-year-old black female with an 18-month history of adult Still's disease developed symptoms and objective findings of restrictive lung disease. The pulmonary function abnormalities persisted unchanged for an additional 18 months despite moderate doses of prednisone. This complication has not been previously described in association with adult Still's disease.
متن کاملClinical and radiological characteristics of patients with late-onset severe restrictive lung defect after hematopoietic stem cell transplantation
BACKGROUND Late-onset noninfectious pulmonary complications (LONIPCs), which occur more than 3 months after allogeneic hematopoietic stem cell transplantation (HSCT), are major causes of morbidity and mortality after transplantation. Among LONIPCs, we occasionally treat patients with late-onset severe restrictive lung defect after HSCT; however, its clinical features have not been fully elucida...
متن کاملCutaneous ulcer in an immunosuppressed patient with adult onset Still's disease: primary cutaneous histoplasmosis?*
Histoplasmosis is caused by the dimorphic fungus Histoplasma capsulatum.Primary infection occurs through inhalation of spores from the air. Immunocompetent individuals are usually asymptomatic, but may develop pulmonary disease. Immunocompromised patients tend to present systemic histoplasmosis with cutaneous lesions occurring by secondary invasion. In this case report, we describe a probable p...
متن کاملEffect of Ultrasound Therapy on Adult-Onset Still\'s Disease: A Case study
Adult-Onset Still's Disease (AOSD) is a rare systemic inflammatory disease of unknown etiology and pathogenesis. AOSD presents in 5% to 10% of patients as Fever of Unknown Origin (FUO) accompanied by systemic manifestations. We reported a compelling case of a 39-year-old African male presenting one-month FUO along with skin rash, sore throat, and arthralgia. After an extensive workup, potential...
متن کاملPulmonary Arterial Hypertension in Adult-Onset Still's Disease: Rapid Response to Anakinra
Adult-onset Still's disease (AOSD) is a rare inflammatory condition characterized by spiking quotidian fever, rash, chronic arthralgia, leukocytosis, and occasional pulmonary involvement such as pleural effusion and transient pulmonary infiltrates. Pulmonary arterial hypertension (PAH) is a rare pulmonary complication of AOSD, and we are aware of only 5 cases reported in the literature. We repo...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- Chest
دوره 92 5 شماره
صفحات -
تاریخ انتشار 1987